Med World +

Adenoma symmetrical sebaceous glands, Pringle’s disease

Adenoma symmetrical sebaceous gland disease Pringle (Adenoma sebaceum symmetricum Pringle) – innate, often a family disease caused by intrauterine developmental disorder of the nervous system and skin (neuroectodermal dysplasia), resulting in formation of ectodermal and mesodermal tumor.
In cases where skin lesions are combined with intellectual disabilities, epilepsy and changes in fundus indicate syndrome Pringle – Burnevilya skin health.

Symptoms.

Numerous hemispherical dense knots zhelttovato red up to lentils, which are usually symmetrically cover the skin of the wings of the nose, nososchechnye, nasolabial folds, chin.
Between the elements, as a rule, there is many telangiectasia, giving a surface area more than a bright red color. In addition to nodular, often observed papillomatoznye growths on the gums, multiple lipomas, fibromas shellfish neck and body skin.
In severe cases, fingers and toes appear hyponychial and okolonogtevye fibromatoznye nodes. The disease begins in childhood and is activated in puberty, often becoming complicated changes of the fundus.
The term “adenoma” should be considered erroneous, because the elements do not have adenomatous structure, but arise as a result of excessive development of the sebaceous glands. Therefore, the disease properly considered as an organ nevi – hamartia.
Differentiated from cystic form of rosacea, aknita, adenoid-cystic epithelioma Brook (acanthoma adenoides cysticum).

Treatment. (more…)

Related posts

• What is dysentery?
• What is a bacterial erysipelas?
• What are foodborne illnesses?
• Sarcoidosis (a disease Besnier-Beck-Shaumann)
• Pulmonary infarction